Hemophilic pseudotumor is a descriptive term which includes any extra-articular osseous destructive and proliferative changes due to spontaneous necrosis of bone by hematoma under pressure. Although only 17 such cases have been reported since 1918, we believe the condition probably is not rare among hemophiliacs.Recognition of this entity is important because of increasing incidence of the hemorrhagic diatheses and their complications.17 The ominous roentgenographic appearance of this lesion, suggestive of osteogenic sarcoma, has repeatedly led to surgical intervention with subsequent hemorrhage, infection, and death.
Our purpose is to report two additional cases of hemophilic pseudotumor occurring in Negro male siblings. By comparing these patients with the previous 17 we hope to outline a useful description of the resorption tumor of bone or pseudotumor of hemophilia. We believe the report is unique as regards race and relationship of these two patients; in other respects it parallels the
ABELL JM, BAILEY RW. Hemophilic PseudotumorTwo Cases Occurring in Siblings. Arch Surg. 1960;81(4):569–581. doi:10.1001/archsurg.1960.01300040053010
Customize your JAMA Network experience by selecting one or more topics from the list below.