A 50-year-old woman was admitted with a mass in the anterior triangle of the neck. Because of interpretation of a needle biopsy specimen as undifferentiated adenocarcinoma, a radical excision of cervical lymph nodes was performed and the specimen showed metastatic adenocarcinoma suggestive of carcinoid tumor. Four months later the patient developed an abdominal mass that turned out to be large mesenteric lymph nodes involved in carcinoid tumor, the primary lesions being in the terminal ileum. Following resection of all visible tumor, the patient has remained symptomatically and chemically well for 15 months. No previous case of carcinoid tumor metastatic to the neck can be found.